Guideline recommendations for diagnosis and clinical management of Ring14 syndrome—first report of an ad hoc task force

被引:0
作者
Berardo Rinaldi
Alessandro Vaisfeld
Sergio Amarri
Chiara Baldo
Giuseppe Gobbi
Pamela Magini
Erto Melli
Giovanni Neri
Francesca Novara
Tommaso Pippucci
Romana Rizzi
Annarosa Soresina
Laura Zampini
Orsetta Zuffardi
Marco Crimi
机构
[1] University of Pavia,Department of Molecular Medicine
[2] Institute of Genomic Medicine,Pediatrics Unit, Department of Women’s and Children’s Health
[3] Catholic University School of Medicine,Medical Genetics Unit, Department of Medical and Surgical Sciences
[4] IRCCS Arcispedale Santa Maria Nuova,Medical Genetics Unit, Department of Woman, Child and Urologic Diseases
[5] Laboratory of Human Genetics,Neurology Unit, Department of Neuro
[6] Galliera Hospital,Motor Diseases
[7] Child Neurology Unit,Department of Psychology
[8] IRCCS Istituto delle Scienze Neurologiche,undefined
[9] S. Orsola-Malpighi University Hospital,undefined
[10] Ospedale S. Anna,undefined
[11] Ambulatorio Oculistica,undefined
[12] AUSL di Reggio Emilia,undefined
[13] S. Orsola-Malpighi University Hospital,undefined
[14] IRCCS Arcispedale Santa Maria Nuova,undefined
[15] Unit of Pediatric Immunology,undefined
[16] Department of Pediatrics,undefined
[17] University of Brescia,undefined
[18] ASST Spedali Civili di Brescia,undefined
[19] University of Milano-Bicocca,undefined
[20] Ring14 International,undefined
[21] Scientific office,undefined
来源
Orphanet Journal of Rare Diseases | / 12卷
关键词
Ring14 syndrome; Recommendations; Caregivers; Best practices; Autistic behavior; Intellectual disability; Seizures; Feeding difficulties; Absent speech; Autism; Malnutrition; Global developmental delay; Growth delay; Abnormality of the face; Abnormality of the retina; Stereotypy; Aggressive behavior; Hyperactivity; Behavioral abnormality; Intellectual disability; Focal seizures; Myoclonus; Hypertelorism; Full cheeks; Horizontal eyebrow; Large forehead; Blepharophimosis; Strabismus; Underdeveloped supraorbital ridges; Thin vermilion border; Epicanthus; Facial asymmetry; Downslanted palpebral fissures; Myopia; Abnormality of retinal pigmentation; Retinal degeneration; Abnormality of the eye; Cataract; Optic neuropathy; Glaucoma; Cafe-au-lait spot; Ventriculomegaly; Short stature; Osteoporosis; Microcephaly; Respiratory tract infection; Abnormality of the corpus callosum; Muscular hypotonia; Celiac disease; Arthritis; Scoliosis, Recurrent infections; Brain atrophy; Osteopenia; Autoimmunity; Status epilepticus; Fever; Encephalopathy; Flexion contracture; Dehydration; Hearing impairment; Recurrent pneumonia; Recurrent upper respiratory tract infections; Pneumonia; Abnormality of vision; Pallor; Astigmatism; Abnormality of skin pigmentation; Respiratory insufficiency; Aspiration; Abnormality of the immune system; Diaphragmatic weakness; Respiratory failure; Dysphagia; Anorexia; Increased body weight; Constipation; Pain; Milia; Focal seizures with impairment of consciousness or awareness; Coloboma; Microphthalmia;
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