Progressive impairment of CaV1.1 function in the skeletal muscle of mice expressing a mutant type 1 Cu/Zn superoxide dismutase (G93A) linked to amyotrophic lateral sclerosis

被引:0
作者
Donald Beqollari
Christin F. Romberg
Gabriella Dobrowolny
Martina Martini
Andrew A. Voss
Antonio Musarò
Roger A. Bannister
机构
[1] University of Colorado School of Medicine,Department of Medicine
[2] La Sapienza University,Cardiology Division
[3] Istituto Italiano di Tecnologia,Institute Pasteur Cenci
[4] College of Science and Mathematics,Bolognetti, DAHFMO
[5] Wright State University,Unit of Histology and Medical Embryology
来源
Skeletal Muscle | / 6卷
关键词
Amyotrophic lateral sclerosis; ALS; Ca; 1.1; Excitation-contraction coupling; L-type; Skeletal muscle; SOD1; Neuromuscular disease;
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