Camurati-Engelmann disease: failure of response to bisphosphonates: report of two cases

被引:0
作者
Glaucio R.W. Castro
Simone Appenzeller
João Francisco Marques-Neto
Manoel B. Bértolo
Adil M. Samara
Ibsen Coimbra
机构
[1] Faculdade de Ciências Médicas/ UNICAMP,Departamento de Clínica Médica
来源
Clinical Rheumatology | 2005年 / 24卷
关键词
Bisphosphonates; Camurati-Engelmann disease; Treatment;
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学科分类号
摘要
Camurati-Engelmann disease is a rare bone disorder characterized by cortical thickening of the diaphysis of tubular bones, with sparing of the epiphysis. It has variable degrees of penetrance and expression, but may be very disabling for the affected individuals who manifest the painful symptoms. The authors report on two women with typical presentation of severe Camurati-Engelmann disease whose treatment with bisphosphonates failed to add any improvement beyond that elicited by corticosteroids alone.
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页码:398 / 401
页数:3
相关论文
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