Primary desmoplastic small round cell tumor of the duodenum

被引：0
作者：
Qi Liu
Nan Liu
DeXing Chen
机构：
[1] Qian Wei Hospital of Jilin province,General Surgery Department
来源：
European Journal of Medical Research | / 19卷
关键词：
chemotherapy; desmoplastic small round cell tumor; duodenum; surgery;
D O I：
暂无
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学科分类号：
摘要：
The desmoplastic small round cell tumor (DSRCT) is an extremely rare tumor that mainly affects adolescents and mostly involves the abdominal and pelvic peritoneum. A 14-year-old girl presented with intermittent epigastric pain; abdominal computed tomography and upper gastrointestinal barium X-ray revealed an 8 cm × 10 cm space-occupying mass in the duodenal region. The patient underwent pancreaticoduodenectomy and the final pathologic diagnosis was DSRCT. Although multi-agent systemic chemotherapy was given, the patient died of metastasis 8 months later. Early diagnosis and surgical treatment with adjuvant chemotherapy seems to be the best treatment choice for this disease.
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  • [1] Gerald WL(1989)Desmoplastic small cell tumor with divergent differentiation Pediatr Pathol 9 177-183
  • [2] Rosai J(2009)A case of desmoplastic small round cell diagnosed in a young female patient Cancer Res Treat 41 233-236
  • [3] Kim JW(1999)A combined cytogenetic and molecular approach to diagnosis in a case of desmoplastic small round cell tumor with a complex translocation (11;22;21) Cancer Genet Cytogenet 108 19-25
  • [4] Park JH(1998)Desmoplastic small round cell tumor: I. a histopathologic study of 39 cases with emphasis on unusual histological patterns Am J Surg Pathol 22 1303-1313
  • [5] Cho HJ(2007)Combined resection and multi-agent adjuvant chemotherapy for intra-abdominal desmoplastic small round cell tumour: case report and review of the literature G Chir 28 367-370
  • [6] Kwon JH(2003)Desmoplastic small round cell tumour: a description of two cases and review of the literature Oncology 64 14-17
  • [7] Koh Y(1996)Desmoplastic small round cell tumors: results of a four-drug chemotherapy regimen in five adult patients Cancer 77 1363-1366
  • [8] Kim SJ(2010)Sequential intensified chemotherapy with stem cell rescue for children and adolescents with desmoplastic small round-cell tumor Bone Marrow Transplant 45 907-911
  • [9] Kim SH(2010)Novel treatment for desmoplastic small round cell tumor: hyperthermic intraperitoneal perfusion J Pediatr Surg 5 1000-1006
  • [10] Lee SH(undefined)undefined undefined undefined undefined-undefined
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