Primary desmoplastic small round cell tumor of the duodenum

被引：0
作者：
Qi Liu
Nan Liu
DeXing Chen
机构：
[1] Qian Wei Hospital of Jilin province,General Surgery Department
来源：
European Journal of Medical Research | / 19卷
关键词：
chemotherapy; desmoplastic small round cell tumor; duodenum; surgery;
D O I：
暂无
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学科分类号：
摘要：
The desmoplastic small round cell tumor (DSRCT) is an extremely rare tumor that mainly affects adolescents and mostly involves the abdominal and pelvic peritoneum. A 14-year-old girl presented with intermittent epigastric pain; abdominal computed tomography and upper gastrointestinal barium X-ray revealed an 8 cm × 10 cm space-occupying mass in the duodenal region. The patient underwent pancreaticoduodenectomy and the final pathologic diagnosis was DSRCT. Although multi-agent systemic chemotherapy was given, the patient died of metastasis 8 months later. Early diagnosis and surgical treatment with adjuvant chemotherapy seems to be the best treatment choice for this disease.
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