ERG assessment of altered retinal function in canine models of retinitis pigmentosa and monitoring of response to translatable gene augmentation therapy

[1] Petersen-Jones SM(2018)Patients and animal models of CNGβ1-deficient retinitis pigmentosa support gene augmentation approach J Clin Invest 128 190-206

[2] Occelli LM(2015)Dog models for blinding inherited retinal dystrophies Hum Gene Ther Clin Dev 26 15-26

[3] Winkler PA(2020)Large animal models of inherited retinal degenerations: a review Cells 20 450-459

[4] Lee W(2017)Characterization of a novel form of progressive retinal atrophy in Whippet dogs: a clinical, electroretinographic, and breeding study Vet Ophthalmol 28 92-95

[5] Sparrow JR(2017)Gene supplementation rescues rod function and preserves photoreceptor and retinal morphology in dogs, leading the way towards treating human PDE6A-retinitis pigmentosa Hum Gene Ther 14 2518-2527

[6] Tsukikawa M(2001)Gene therapy restores vision in a canine model of childhood blindness Nat Genet 9 e90390-138

[7] Boye SL(2008)Topographical characterization of cone photoreceptors and the area centralis of the canine retina Mol Vis 50 801-465

[8] Chiodo V(2014)Canine retina has a primate fovea-like bouquet of cone photoreceptors which is affected by inherited macular degenerations PLoS ONE 8 e72229-435

[9] Capasso JE(2009)Characterization of a canine model of autosomal recessive retinitis pigmentosa due to a Invest Ophthalmol Vis Sci 25 130-61

[10] Becirovic E(2013) mutation PLoS ONE 60 465-12

[1] Petersen-Jones SM(2018)Patients and animal models of CNGβ1-deficient retinitis pigmentosa support gene augmentation approach J Clin Invest 128 190-206

[2] Occelli LM(2015)Dog models for blinding inherited retinal dystrophies Hum Gene Ther Clin Dev 26 15-26

[3] Winkler PA(2020)Large animal models of inherited retinal degenerations: a review Cells 20 450-459

[4] Lee W(2017)Characterization of a novel form of progressive retinal atrophy in Whippet dogs: a clinical, electroretinographic, and breeding study Vet Ophthalmol 28 92-95

[5] Sparrow JR(2017)Gene supplementation rescues rod function and preserves photoreceptor and retinal morphology in dogs, leading the way towards treating human PDE6A-retinitis pigmentosa Hum Gene Ther 14 2518-2527

[6] Tsukikawa M(2001)Gene therapy restores vision in a canine model of childhood blindness Nat Genet 9 e90390-138

[7] Boye SL(2008)Topographical characterization of cone photoreceptors and the area centralis of the canine retina Mol Vis 50 801-465

[8] Chiodo V(2014)Canine retina has a primate fovea-like bouquet of cone photoreceptors which is affected by inherited macular degenerations PLoS ONE 8 e72229-435

[9] Capasso JE(2009)Characterization of a canine model of autosomal recessive retinitis pigmentosa due to a Invest Ophthalmol Vis Sci 25 130-61

[10] Becirovic E(2013) mutation PLoS ONE 60 465-12