Pseudomyxoma peritonei - A revisit: Report of 2 cases and literature review

被引：17

作者：

Li C. ^{[1
]}

Kanthan R. ^{[1
]}

Kanthan S.C. ^{[2
]}

机构：

[1] Department of Pathology, Royal University Hospital, Saskatoon, SK S7N 0W8, 103, Hospital Drive

[2] Department of Surgery, Royal University Hospital, Saskatoon, SK S7N 0W8, 103, Hospital Drive

来源：

World Journal of Surgical Oncology | / 4卷 / 1期

关键词：

Mucinous Neoplasm; Intraperitoneal Chemotherapy; Pseudomyxoma Peritonei; Mucinous Cystadenocarcinoma; Appendiceal Tumor;

D O I：

10.1186/1477-7819-4-60

中图分类号：

学科分类号：

摘要：

Background: Pseudomyxoma peritonei (PMP) is a rare, chronic, relapsing, diagnostically challenging and poorly understood disease characterized by disseminated mucinous ascites and peritoneal implants. Case presentation: We report two cases of PMP that represent the two biological variants of disseminated peritoneal adenomucinosis (DPAM) - the benign variant and the peritoneal mucinous carcinomatosis (PMCA) - the malignant variant, both of which were characterized by multiple relapses and progression of the disease despite aggressive management. Conclusion: Even with a better understanding and recent advances in the management of these cases, PMP remains an enigmatic disease with a protracted clinical course characterized by multiple recurrences despite surgery and/or chemotherapy. Recognition of PMP as a delayed consequence years later should alert all surgeons to be extremely vigilant when treating mucinous neoplasms of the appendix, with special care being directed towards adequate excision and thorough debridement at the initial diagnosis. © 2006 Li et al; licensee BioMed Central Ltd.

引用

共 22 条

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[2]

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[3]

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[10]

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