Endovascular Treatment of a Carotid Dissecting Pseudoaneurysm in a Patient with Ehlers-Danlos Syndrome Type IV with Fatal Outcome

被引：0
作者：
Siok Ping Lim
Martin J. Duddy
机构：
[1] Selly Oak Hospital,Department of Radiology
[2] University Hospital,undefined
[3] Birmingham NHS Foundation Trust,undefined
来源：
CardioVascular and Interventional Radiology | 2008年 / 31卷
关键词：
Dissection; Pseudoaneurysm; Carotid artery; Covered stent; Endovascular treatment; Ehlers-Danlos syndrome;
D O I：
暂无
中图分类号：
学科分类号：
摘要：
We present a patient with Ehlers-Danlos syndrome type IV (EDS IV) with a carotid dissecting pseudoaneurysm causing severe carotid stenosis. This lesion was treated endovascularly. Unfortunately, the patient died of remote vascular catastrophes (intracranial hemorrhage and abdominal aortic rupture). This unique case illustrates the perils of endovascular treatment of EDS IV patients and the need for preoperative screening for concomitant lesions. It also shows that a dissecting pseudoaneurysm can feasibly be treated with a covered stent and that closure is effective using Angioseal in patients with EDS IV.
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页码：201 / 204
页数：3
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[1]  
Smith LT(1997)Mutations in the COL3A1 gene result in the Ehlers-Danlos syndrome type IV and alterations in the size and distribution of the major collagen fibrils of the dermis J Invest Dermatol 108 241-247
[2]  
Schwarze U(2004)Increased carotid wall stress in vascular Ehlers-Danlos syndrome Circulation 109 1530-1535
[3]  
Goldstein J(2005)The spectrum, management and clinical outcome of Ehlers-Danlos syndrome type IV: a 30-year experience J Vasc Surg 42 98-106
[4]  
Boutouyrie P(1998)Ehlers-Danlos syndromes: revised nosology, Villefranche, 1997. Ehlers-Danlos National Foundation (USA) and Ehlers-Danlos Support Group (UK) Am J Med Genet 77 31-37
[5]  
Germain DP(2003)Emergent endovascular treatment of a spontaneous internal carotid artery dissection with pseudoaneurysm J Endovasc Ther 10 643-646
[6]  
Fiessinger JN(2001)Pseudoaneurysm of the internal carotid artery: treatment with a covered stent Cardiovasc Interv Radiol 24 283-285
[7]  
Oderich GS(2000)Remote vascular catastrophes after neurovascular interventional therapy for type 4 Ehlers-Danlos syndrome Am J Neuroradiol 21 974-976
[8]  
Panneton JM(2006)Fatal peritoneal bleeding following embolization of a carotid-cavernous fistula in Ehlers-Danlos syndrome type IV Cardiovasc Interv Radiol 29 1104-1106
[9]  
Bower TC(2003)Successful stent placement for cervical artery dissection associated with the Ehlers-Danlos syndrome. Case report and review of the literature J Neurosurg 99 1077-1081
[10]  
Beighton P(2006)Resolution of large azygos vein aneurysm following stent-graft shunt placement in a patient with Ehlers-Danlos syndrome type IV Cardiovasc Interv Radiol 29 915-919
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