Nevoid Basal Cell Carcinoma Syndrome: A Case Report and Review

被引：4

作者：

Bala Subramanyam S. ^{[1
]}

Naga Sujata D. ^{[1
]}

Sridhar K. ^{[2
]}

Pushpanjali M. ^{[1
]}

机构：

[1] Department of Oral and Maxillofacial Surgery, Government Dental College and Hospital, RIMS, Kadapa, Andhra Pradesh

[2] Department of General Pathology, RIMS, Kadapa, Andhra Pradesh

来源：

Journal of Maxillofacial and Oral Surgery | 2015年 / 14卷 / Suppl 1期

关键词：

Goltz syndrome; Gorlin; Keratocystic odontogenic tumor; NBCCS;

D O I：

10.1007/s12663-011-0262-5

中图分类号：

学科分类号：

摘要：

Nevoid basal cell carcinoma syndrome, a rare autosomal dominant disorder, comprises of a number of abnormalities such as multiple nevoid basal cell carcinomas, skeletal abnormalities and multiple keratocystic odontogenic tumors. Diagnosis may be difficult because of the variability of expressivity and different ages of onset for different traits of this disorder. The dental clinician may be the first to encounter and identify this syndrome, when the multiple cysts like radiolucencies are discovered on panoramic view. This article reports a case of Nevoid basal cell carcinoma syndrome and provides an overview on diagnosis and management. © 2011, Association of Oral and Maxillofacial Surgeons of India.

引用

页码：11 / 15

页数：4

共 16 条

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