Mayer-Rokitansky syndrome and anorectal malformation

被引：6

作者：

Patankar S.P. ^{[1
,4
]}

Kalrao V. ^{[2
]}

Patankar S.S. ^{[3
]}

机构：

[1] Department of Pediatric Surgery, Bharati Vidyapith Deemed University, Bharati Medical College, Pune

[2] Department of Pediatrics, Bharati Vidyapith Deemed University, Bharati Medical College, Pune

[3] Department of General Surgery, Bharati Vidyapith Deemed University, Bharati Medical College, Pune

[4] Padmadarshan Co-op Socy, Pune: 411 009. Maharashtra, S. No. 62/B, Off Satara road

来源：

The Indian Journal of Pediatrics | 2004年 / 71卷 / 12期

关键词：

Anorectal malformation; Mayer Rokitansky syndrome; Renal agenesis; Vaginoplasty;

D O I：

10.1007/BF02829831

中图分类号：

学科分类号：

摘要：

Mayer Rokitansky Kuster Houser syndrome (MRKH syndrome) is characterized by Mullerian duct structures agenesis, vaginal atresia being the commonest variant. It can be associated with renal, skeletal, spine and other malformations. Patient with Mayer Rokitansky syndrome has a varied presentation from newborn period to adolescence. Thorough investigations are required for classification of the syndrome and diagnosis of associated anomalies. The MRKH syndrome patient may require complex vaginal reconstructive surgery and a detailed counseling about the potentials of menstruation and fertility. Here we are presenting a patient having association of anorectal malformation, Mullerian duct agenesis and renal anomaly.

引用

页码：1133 / 1135

页数：2

共 18 条

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