Intractable itch relieved by 4-phenylbutyrate therapy in patients with progressive familial intrahepatic cholestasis type 1

被引:0
作者
Yasuhiro Hasegawa
Hisamitsu Hayashi
Sotaro Naoi
Hiroki Kondou
Kazuhiko Bessho
Koji Igarashi
Kentaro Hanada
Kie Nakao
Takeshi Kimura
Akiko Konishi
Hironori Nagasaka
Yoko Miyoshi
Keiichi Ozono
Hiroyuki Kusuhara
机构
[1] Osaka University Graduate School of Medicine,Department of Pediatrics
[2] The University of Tokyo,Laboratory of Molecular Pharmacokinetics, Graduate School of Pharmaceutical Sciences
[3] TOSOH Corporation,Bioscience Division, Reagent Development Department
[4] National Institute of Infectious Diseases,Department of Biochemistry and Cell Biology
[5] 1-23-1,Department of Pediatrics
[6] Toyama,undefined
[7] Takarazuka City Hospital,undefined
[8] 4-5-1 Kohama,undefined
来源
Orphanet Journal of Rare Diseases | / 9卷
关键词
Pediatric liver disease; Cholestasis; PFIC1; Pruritus; 4PB;
D O I
暂无
中图分类号
学科分类号
摘要
引用
收藏
相关论文
共 307 条
  • [51] Hoeben KA(undefined)undefined undefined undefined undefined-undefined
  • [52] van Marle J(undefined)undefined undefined undefined undefined-undefined
  • [53] Pawlikowska L(undefined)undefined undefined undefined undefined-undefined
  • [54] Bull LN(undefined)undefined undefined undefined undefined-undefined
  • [55] Hofmann AF(undefined)undefined undefined undefined undefined-undefined
  • [56] Knisely AS(undefined)undefined undefined undefined undefined-undefined
  • [57] Oude Elferink RP(undefined)undefined undefined undefined undefined-undefined
  • [58] Byrne JA(undefined)undefined undefined undefined undefined-undefined
  • [59] Strautnieks SS(undefined)undefined undefined undefined undefined-undefined
  • [60] Mieli-Vergani G(undefined)undefined undefined undefined undefined-undefined