Intractable itch relieved by 4-phenylbutyrate therapy in patients with progressive familial intrahepatic cholestasis type 1

被引:0
作者
Yasuhiro Hasegawa
Hisamitsu Hayashi
Sotaro Naoi
Hiroki Kondou
Kazuhiko Bessho
Koji Igarashi
Kentaro Hanada
Kie Nakao
Takeshi Kimura
Akiko Konishi
Hironori Nagasaka
Yoko Miyoshi
Keiichi Ozono
Hiroyuki Kusuhara
机构
[1] Osaka University Graduate School of Medicine,Department of Pediatrics
[2] The University of Tokyo,Laboratory of Molecular Pharmacokinetics, Graduate School of Pharmaceutical Sciences
[3] TOSOH Corporation,Bioscience Division, Reagent Development Department
[4] National Institute of Infectious Diseases,Department of Biochemistry and Cell Biology
[5] 1-23-1,Department of Pediatrics
[6] Toyama,undefined
[7] Takarazuka City Hospital,undefined
[8] 4-5-1 Kohama,undefined
来源
Orphanet Journal of Rare Diseases | / 9卷
关键词
Pediatric liver disease; Cholestasis; PFIC1; Pruritus; 4PB;
D O I
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