Anesthesia management in living-donor liver transplantation in a patient with carbamoyl phosphate synthetase deficiency: a case report

被引:0
作者
Hiroki Matsushita
Tetsushiro Fujiyoshi
Koichiro Yoshimaru
Toshiharu Matsuura
Yuichi Mushimoto
Yuji Karashima
Ken Yamaura
机构
[1] Kyushu University Hospital,Department of Anesthesiology and Critical Care Medicine
[2] Kyushu University Hospital,Department of Pediatric Surgery
[3] Kyushu University Hospital,Department of Pediatrics
来源
JA Clinical Reports | / 8卷
关键词
Pediatric; Urea cycle disorders; UCD; Carbamoyl phosphate synthetase deficiency; CPS1D; Hyperammonemia; Living-donor liver transplantation;
D O I
暂无
中图分类号
学科分类号
摘要
引用
收藏
相关论文
共 81 条
[11]  
Rubio P(2012)Suggested guidelines for the diagnosis and management of urea cycle disorders Orphanet J Rare Dis 7 0-1
[12]  
Nakamura K(2010)Living-donor liver transplantation for carbamoyl phosphate synthetase 1 deficiency Pediatric Transplant 14 1036-1040
[13]  
Kido J(2019)Red blood cell transfusion in pediatric orthotopic liver transplantation: what a difference a few decades make Anesth Analg. 129 1087-1092
[14]  
Mitsubuchi H(1982)The concentration of ammonia in blood and plasma stored for transfusion Resuscitation 10 135-139
[15]  
Endo F(2001)The effect of storage on ammonia concentration in canine packed red blood cells J Vet Emerg Crit Care 11 23-26
[16]  
Desborough JP(2013)Increased red blood cell transfusions are associated with worsening outcomes in pediatric heart transplant patients Anesth Analgesia. 116 1295-1308
[17]  
Igarashi M(2016)Relationship between transfusion volume and outcomes in children undergoing noncardiac surgery Transfusion. 56 2487-2494
[18]  
Kawana S(undefined)undefined undefined undefined undefined-undefined
[19]  
Iwasaki H(undefined)undefined undefined undefined undefined-undefined
[20]  
Namiki A(undefined)undefined undefined undefined undefined-undefined