Anesthesia management in living-donor liver transplantation in a patient with carbamoyl phosphate synthetase deficiency: a case report

被引:0
作者
Hiroki Matsushita
Tetsushiro Fujiyoshi
Koichiro Yoshimaru
Toshiharu Matsuura
Yuichi Mushimoto
Yuji Karashima
Ken Yamaura
机构
[1] Kyushu University Hospital,Department of Anesthesiology and Critical Care Medicine
[2] Kyushu University Hospital,Department of Pediatric Surgery
[3] Kyushu University Hospital,Department of Pediatrics
来源
JA Clinical Reports | / 8卷
关键词
Pediatric; Urea cycle disorders; UCD; Carbamoyl phosphate synthetase deficiency; CPS1D; Hyperammonemia; Living-donor liver transplantation;
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