Paratesticular pleomorphic rhabdomyosarcoma in an adult

被引:8
作者
Demir A. [1 ]
Önol F.F. [1 ]
Türkeri L. [1 ]
机构
[1] Department of Urology, Marmara University Hospital, Altunizade 34662 Istanbul
关键词
Multidisciplinary approach; Paratesticular rhabdomyosarcoma; Poor prognosis;
D O I
10.1007/s11255-004-0853-x
中图分类号
学科分类号
摘要
Rhabdomyosarcoma (RMS) is the commonest variety of soft tissue sarcoma in children and young adults. It represents 6.5% of all malignant tumours in paediatrics with an annual incidence of 4 to 7 cases/million children. The primary paratesticular site is considered to have a good prognosis in comparison with other rhabdomyosarcomas, despite the frequency of retroperitoneal lymph node invasion. This superficial site allows rapid diagnosis and consequently often complete resection of the tumor. The multi- disciplinary treatment of paratesticular RMS has improved control of the disease with a 2-year survival of 80%. We herein report a case with paratesticular pleomorphic RMS, a rare and prognostically unfavorable variant of RMS, who is disease free for 60 months after management with multidisciplinary approach. © 2004 Kluwer Academic Publishers.
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页码:577 / 578
页数:1
相关论文
共 8 条
[1]  
Shapiro E., Strother D., Pediatric genitourinary rhabdomyosarcoma, J. Urol., 148, (1992)
[2]  
Elsasser E., Tumours of the epididymis, Recent Results Cancer Res., 40, pp. 163-175, (1970)
[3]  
Snyder III H.M., D'Angio G.J., Evans A.E., Raney R.B., Pediatric oncology, Campbell's Urology, 2, pp. 2210-2256, (1998)
[4]  
Maurer H.M., Gehan E.A., Beltangady M., Et al., The intergroup rhabdomyosarcoma study - II, Cancer, 71, (1993)
[5]  
Blitzer P., Dosoretz D., Proppe K., Shipley W., Treatment of malignant tumours of the spermatic cord: A study of 10 cases and review of the literature, J. Urol., 126, (1981)
[6]  
Banowsky L., Shultz G., Sarcoma of the spermatic cord and tunics: Review of the literature, case report and discussion of the role of retroperitoneal lymph node dissection, J. Urol., 103, (1970)
[7]  
Catton C.N., Cummings B.J., Fornasier V., Et al., Adult paratesticular sarcomas: A review of 21 cases, J. Urol., 146, (1991)
[8]  
Adjuvant chemotherapy for localized resectable soft-tissue sarcoma of adults: Meta-analysis of individual data, Lancet, 350, (1997)