Intestinal bleeding from arteriovenous malformations of the small bowel in a patient with Cowden syndrome: report of a case

被引：0
作者：
Yoshifumi Nakayama
Jun Segawa
Kazufumi Sujita
Noritaka Minagawa
Takayuki Torigoe
Masanori Hisaoka
Koji Yamaguchi
机构：
[1] University of Occupational and Environmental Health,Department of Surgery, School of Medicine
[2] Wakamatsu Hospital of University of Occupational and Environmental Health,Department of Gastroenterological and General Surgery
[3] Hagiwara Central Hospital,Department of Cardiovascular Medicine
[4] Hagiwara Central Hospital,Department of Gastroenterology
[5] University of Occupational and Environmental Health,Department of Pathology and Oncology, School of Medicine
来源：
Surgery Today | 2013年 / 43卷
关键词：
Cowden syndrome; Arterial venous malformations; Gastrointestinal bleeding; Gastrointestinal polyposis;
D O I：
暂无
中图分类号：
学科分类号：
摘要：
This report presents the case of a patient with Cowden syndrome who had arteriovenous malformations (AVMs) at the jejunum and the ileum and experienced intestinal bleeding. A 54-year-old Japanese male presented with general fatigue and melena. Endoscopic examinations showed gastrointestinal polyposis from the esophagus to the rectum. However, the site of bleeding was not identified. There were some papules on his face and neck. He also had macrocephaly and had multiple papillomas along the gum-line. These findings indicated a clinical diagnosis of Cowden syndrome. Enhanced computed tomography (CT) and angiography analyses indicated the presence of AVMs at the jejunum and the ileum. He was treated with partial resection of the jejunum and ileum including these two AVMs. This was a rare case of two AVMs involving the small bowel in a patient with Cowden syndrome. Enhanced CT was very useful and convenient for the detection of gastrointestinal AVMs in this case.
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页码：542 / 546
页数：4
相关论文
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