The surgical management of fibrous dysplasia of bone

被引：0
作者：
Robert P Stanton
Ernesto Ippolito
Dempsey Springfield
Lynn Lindaman
Shlomo Wientroub
Arabella Leet
机构：
[1] Nemours Children’s Clinic,Pediatric Orthopedics
[2] University of Rome Tor Vergata,Department of Orthopedic Surgery
[3] Harvard University,Massachusetts General Hospital
[4] Lindaman Orthopedics Des Moines,Dana Children’s Hospital
[5] Tel Aviv University,undefined
[6] Johns Hopkins University,undefined
来源：
Orphanet Journal of Rare Diseases | / 7卷
关键词：
Fibrous Dysplasia; Aneurysmal Bone Cyst; Limb Length Discrepancy; Bone Deformity; Lower Extremity Fracture;
D O I：
暂无
中图分类号：
学科分类号：
摘要：
The surgical management of Polyostotic Fibrous Dysplasia (FD) of bone is technically demanding. The most effective methods to manage the associated bone deformity remain unclear. The marked variation in the degree and pattern of bone involvement has made it difficult to acquire data to guide the surgeon’s approach to these patients. In light of the paucity of data, but need for guidance, recognized experts in the management of these patients came together at the National Institutes of Health in Bethesda, Maryland as part of an International meeting to address issues related to fibrous dysplasia of bone to discuss and refine their recommendations regarding the surgical indications and preferred methods for the management of these challenging patients. The specific challenges, recommended approaches, and “lessons learned” are presented in hopes that surgeons faced with typical deformities can be guided in the surgical reconstruction of both children and adults with FD.
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