Erdheim-Chester disease with multisystem involvement in a 4-year-old

被引：0

作者：

Sook Yun Song

Sun Wha Lee

Kyung-ha Ryu

Sun Hee Sung

机构：

[1] Ewha Womans University School of Medicine,Department of Radiology

[2] Ewha Womans University Mokdong Hospital,Department of Radiology

[3] Ewha Womans University School of Medicine,Department of Pediatrics

[4] Ewha Womans University School of Medicine,Department of Pathology

来源：

Pediatric Radiology | 2012年 / 42卷

关键词：

Erdheim-Chester disease; Histiocytosis; Child;

D O I：

暂无

中图分类号：

学科分类号：

摘要：

Erdheim-Chester disease is a rare form of non-Langerhans histiocytosis of unknown origin occurring mainly in adults. It is extremely rare in children. We report a case of a 4-year-old boy with Erdheim-Chester disease that initially presented as hemifacial palsy and bone pain with multisystem involvement. We describe radiographic findings of bones that show characteristic bilateral symmetrical osteosclerosis with atypical osteolytic lesions in addition to CT findings for pulmonary involvement and MR findings for intracranial lesions.

引用

页码：632 / 635

页数：3

共 24 条

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[10]

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