Current Concepts in Management of Vestibular Schwannomas in Neurofibromatosis Type 2

被引：1

作者：

Tysome J.R. ^{[1
]}

Axon P.R. ^{[1
]}

Donnelly N.P. ^{[1
]}

Durie-Gair J. ^{[1
]}

Gareth Evans D. ^{[2
]}

Ferner R.E. ^{[3
]}

Macfarlane R. ^{[4
]}

Mannion R. ^{[4
]}

Nduka C. ^{[5
]}

Morris K. ^{[6
]}

Pretorius P.M. ^{[7
]}

Rands G. ^{[8
]}

Rowe J. ^{[9
]}

Taylor A. ^{[10
]}

机构：

[1] Departments of Otolaryngology, Cambridge University Hospitals NHS Foundation Trust, Cambridge

[2] Departments of Genetics, Manchester Royal Infirmary, Manchester

[3] Neurofibromatosis Centre, Guy’s and St. Thomas’ NHS Foundation Trust, London

[4] Departments of Neurosurgery, Cambridge University Hospitals NHS Foundation Trust, Cambridge

[5] Department of Plastic Surgery, East Grinstead Hospital, West Sussex

[6] Departments of Neurology, John Radcliffe Hospital, Oxford

[7] Departments of Neuroradiology, John Radcliffe Hospital, Oxford

[8] Departments of Psychology, Cambridge University Hospitals NHS Foundation Trust, Cambridge

[9] Department of Neurosurgery, Sheffield Gamma Knife Centre, Royal Hallamshire Hospital, Sheffield

[10] Departments of Genetics, Cambridge University Hospitals NHS Foundation Trust, Cambridge

来源：

Current Otorhinolaryngology Reports | 2014年 / 2卷 / 4期

关键词：

Multidisciplinary; Neurofibromatosis type 2; Vestibular schwannoma;

D O I：

10.1007/s40136-014-0067-4

中图分类号：

学科分类号：

摘要：

Neurofibromatosis type 2 (NF2) is an autosomal dominant condition resulting in multiple benign intracranial and spinal tumours including bilateral vestibular schwannomas. The management of vestibular schwannomas in NF2 is particularly challenging, given the young presentation of many patients, the natural history of the disease that often leads to complete loss of hearing in both ears and the burden of other tumours. Specialists from multidisciplinary NF2 teams describe current concepts in the management of vestibular schwannomas in NF2. © 2014, Springer Science+Business Media New York.

引用

页码：248 / 255

页数：7

共 40 条

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