MR imaging of arrhythmogenic right ventricular dysplasia

Arrhythmogenic right ventricular displasia (ARVD) is a heart disease characterized by a total or partial fat replacement of the myocardium. Echocardiography, which has been most commonly used for the diagnosis of ARVD, usually only demonstrates right ventricular enlargement with associated hypokinesia and with normal left ventricular chamber size. Angiocardiography is very effective in the evaluation of ARVD, especially, in the detection of wall motion abnormalities and bulgings. However, angiocardiography is invasive. Magnetic resonance imaging is a non-invasive, repeatable technique, which allows a more accurate evaluation of the right ventricular chamber and free wall. Therefore MRI is very effective in the differentiation of the high signal intensity of the fat from other medium intensity tissue, such as muscle, and in detection of fibro-fatty replacement of myocardium. It provides an accurate assessment of right-chamber enlargement, right ventricle outflow tract ectasia and wall motion abnormalities by cine-MR GE technique.