Effects of sirolimus in lymphangioleiomyomatosis patients on lung cysts and pulmonary function: long-term follow-up observational study

[1] Harknett EC(2011)Use of variability in national and regional data to estimate the prevalence of lymphangioleiomyomatosis QJM 104 971-979

[2] Chang WY(2011)Imaging features of lymphangioleiomyomatosis: diagnostic pitfalls AJR Am J Roentgenol 196 982-986

[3] Byrnes S(1995)Pulmonary lymphangioleiomyomatosis: a report of 46 patients including a clinicopathologic study of prognostic factors Am J Respir Crit Care Med 151 527-533

[4] Avila NA(1990)Lymphangioleiomyomatosis. Clinical course in 32 patients N Engl J Med 323 1254-1260

[5] Dwyer AJ(2010)Regulation of the mTOR complex 1 pathway by nutrients, growth factors, and stress Mol Cell 40 310-322

[6] Moss J(2007)Molecular pathogenesis of lymphangioleiomyomatosis: lessons learned from orphans Am J Respir Cell Mol Biol 36 398-408

[7] Kitaichi M(1999)Decline in lung function in lymphangioleiomyomatosis: relation to menopause and progesterone treatment Am J Respir Crit Care Med 160 628-633

[8] Nishimura K(2004)Decline in lung function in patients with lymphangioleiomyomatosis treated with or without progesterone Chest 126 1867-1874

[9] Itoh H(2004)Survival and disease progression in UK patients with lymphangioleiomyomatosis Thorax 59 800-803

[10] Izumi T(2016)A novel quantitative computed tomographic analysis suggests how sirolimus stabilizes progressive air trapping in lymphangioleiomyomatosis Ann Am Thorac Soc 13 342-349

[1] Harknett EC(2011)Use of variability in national and regional data to estimate the prevalence of lymphangioleiomyomatosis QJM 104 971-979

[2] Chang WY(2011)Imaging features of lymphangioleiomyomatosis: diagnostic pitfalls AJR Am J Roentgenol 196 982-986

[3] Byrnes S(1995)Pulmonary lymphangioleiomyomatosis: a report of 46 patients including a clinicopathologic study of prognostic factors Am J Respir Crit Care Med 151 527-533

[4] Avila NA(1990)Lymphangioleiomyomatosis. Clinical course in 32 patients N Engl J Med 323 1254-1260

[5] Dwyer AJ(2010)Regulation of the mTOR complex 1 pathway by nutrients, growth factors, and stress Mol Cell 40 310-322

[6] Moss J(2007)Molecular pathogenesis of lymphangioleiomyomatosis: lessons learned from orphans Am J Respir Cell Mol Biol 36 398-408

[7] Kitaichi M(1999)Decline in lung function in lymphangioleiomyomatosis: relation to menopause and progesterone treatment Am J Respir Crit Care Med 160 628-633

[8] Nishimura K(2004)Decline in lung function in patients with lymphangioleiomyomatosis treated with or without progesterone Chest 126 1867-1874

[9] Itoh H(2004)Survival and disease progression in UK patients with lymphangioleiomyomatosis Thorax 59 800-803

[10] Izumi T(2016)A novel quantitative computed tomographic analysis suggests how sirolimus stabilizes progressive air trapping in lymphangioleiomyomatosis Ann Am Thorac Soc 13 342-349