Nutrition management of PKU with pegvaliase therapy: update of the web-based PKU nutrition management guideline recommendations

被引：0
|
作者：
Amy Cunningham
Fran Rohr
Patricia Splett
Shideh Mofidi
Heather Bausell
Adrya Stembridge
Aileen Kenneson
Rani H. Singh
机构：
[1] Tulane University School of Medicine,Hayward Genetics Center
[2] Splett and Associates,Maria Fareri Children’s Hospital/Westchester
[3] New York Medical College,Department of Human Genetics
[4] Ann and Robert H. Lurie Children’s Hospital of Chicago,undefined
[5] Emory University,undefined
来源：
Orphanet Journal of Rare Diseases | / 18卷
关键词：
Phenylketonuria; PKU; Phenylalanine ammonia lyase; Pegvaliase; Palynziq®; Nutrition guideline; Nutrition;
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