Anesthetic management for foramen magnum decompression in a patient with Morquio syndrome: a case report

被引：0
作者：
Lakshminarsimhaiah Geetha
Muthuchellappan Radhakrishnan
Biligiri Sridhar Raghavendra
G. S. Umamaheswara Rao
Bhagavatula Indira Devi
机构：
[1] National Institute of Mental Health and Neurosciences (NIMHANS),Department of Neuroanesthesia
[2] National Institute of Mental Health and Neurosciences (NIMHANS),Department of Neurosurgery
来源：
Journal of Anesthesia | 2010年 / 24卷
关键词：
Mucopolysaccharidosis; Difficult airway; Fiberoptic intubation; Cervical myelopathy; Atlantoaxial dislocation;
D O I：
暂无
中图分类号：
学科分类号：
摘要：
Morquio syndrome is a hereditary mucopolysaccharide disorder presenting with an abnormality of the craniocervical junction from childhood. We describe an adult patient who presented with Morquio syndrome who had subglottic narrowing of the airway, restrictive pulmonary disease, and mild mitral regurgitation and trivial aortic regurgitation. The anesthetic management of this patient for atlantoaxial stabilization is presented.
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页码：594 / 597
页数：3
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