Myocardial lipid content in Fabry disease: a combined 1H-MR spectroscopy and MR imaging study at 3 Tesla

被引:0
作者
B. Petritsch
H. Köstler
A. M. Weng
M. Horn
T. Gassenmaier
A. S. Kunz
F. Weidemann
C. Wanner
T. A. Bley
M. Beer
机构
[1] University Hospital Würzburg,Department of Diagnostic and Interventional Radiology
[2] Comprehensive Heart Failure Center,University of Würzburg
[3] Katharinen-Hospital Unna,Department of Internal Medicine II/Cardiology
[4] University Hospital Würzburg,Department of Internal Medicine I
[5] University Hospital Ulm,Department of Diagnostic and Interventional Radiology
来源
BMC Cardiovascular Disorders | / 16卷
关键词
Morbus Fabry; Magnetic resonance spectroscopy; Myocardial lipid content; Rare diseases; Lysosomal storage disease; Late gadolinium enhancement;
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[1]  
Desnick RJ(2006)Fabry disease: clinical spectrum and evidence-based enzyme replacement therapy Nephrol Ther 2 172-185
[2]  
Banikazemi M(1999)Prevalence of lysosomal storage disorders JAMA 281 249-254
[3]  
Meikle PJ(2011)Differences in Fabry cardiomyopathy between female and male patients: consequences for diagnostic assessment JACC Cardiovasc Imaging 4 592-601
[4]  
Hopwood JJ(2001)Natural history of Fabry disease in affected males and obligate carrier females J Inherit Metab Dis 24 13-14
[5]  
Clague AE(2006)Impact of enzyme replacement therapy on cardiac morphology and function and late enhancement in Fabry’s cardiomyopathy Am J Cardiol 97 1515-1518
[6]  
Carey WF(2003)Gadolinium enhanced cardiovascular magnetic resonance in Anderson-Fabry disease. Evidence for a disease specific abnormality of the myocardial interstitium Eur Heart J 24 2151-2155
[7]  
Niemann M(2007)Myocardial late gadolinium enhancement in specific cardiomyopathies by cardiovascular magnetic resonance: a preliminary experience J Cardiovasc Med (Hagerstown) 8 1076-1079
[8]  
Herrmann S(2013)Fibrosis: a key feature of Fabry disease with potential therapeutic implications Orphanet J Rare Dis 8 116-97
[9]  
Hu K(2004)Fabry disease: reduced activities of respiratory chain enzymes with decreased levels of energy-rich phosphates in fibroblasts Mol Genet Metab 82 93-352
[10]  
Breunig F(2014)Natural course of Fabry disease and the effectiveness of enzyme replacement therapy: a systematic review and meta-analysis: Effectiveness of ERT in different disease stages J Inherit Metab Dis 37 341-645