Improving clinical trial design for Duchenne muscular dystrophy

被引:0
作者
Luciano Merlini
Patrizia Sabatelli
机构
[1] Istituto Ortopedico Rizzoli,Laboratory of Musculoskeletal Cell Biology
[2] IRCCS,undefined
[3] CNR National Research Council of Italy,undefined
[4] Institute of Molecular Genetics,undefined
来源
BMC Neurology | / 15卷
关键词
Duchenne muscular dystrophy; Dystrophin evaluation; Clinical trial; Corticosteroid treatment; Exon skipping; Splice modulation;
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[1]  
Hoffman EP(2014)Exon-skipping therapy: a roadblock, detour, or bump in the road? Sci Transl Med 6 230fs214-2686
[2]  
McNally EM(2007)Local dystrophin restoration with antisense oligonucleotide PRO051 N Engl J Med 357 2677-928
[3]  
van Deutekom JC(2009)Local restoration of dystrophin expression with the morpholino oligomer AVI-4658 in Duchenne muscular dystrophy: a single-blind, placebo-controlled, dose-escalation, proof-of-concept study Lancet Neurol 8 918-996
[4]  
Janson AA(2014)Safety and efficacy of drisapersen for the treatment of Duchenne muscular dystrophy (DEMAND II): an exploratory, randomised, placebo-controlled phase 2 study Lancet Neurol 13 987-1522
[5]  
Ginjaar IB(2011)Systemic administration of PRO051 in Duchenne's muscular dystrophy New Engl J Med 364 1513-26
[6]  
Frankhuizen WS(2015)The emperor's new dystrophin: finding sense in the noise Trends Mol Med 21 417-605
[7]  
Aartsma-Rus A(2011)Exon skipping and dystrophin restoration in patients with Duchenne muscular dystrophy after systemic phosphorodiamidate morpholino oligomer treatment: an open-label, phase 2, dose-escalation study Lancet 378 595-647
[8]  
Bremmer-Bout M(2013)Eteplirsen for the treatment of Duchenne muscular dystrophy Ann Neurol 74 637-487
[9]  
den Dunnen JT(2014)Ataluren treatment of patients with nonsense mutation dystrophinopathy Muscle Nerve 50 477-239
[10]  
Koop K(2013)Phase 2a study of ataluren-mediated dystrophin production in patients with nonsense mutation Duchenne muscular dystrophy PLoS One 8 e152-329