Cri-du-chat syndrome mimics Silver-Russell syndrome depending on the size of the deletion: a case report

被引:0
作者
Yerai Vado
Javier Errea-Dorronsoro
Isabel Llano-Rivas
Nerea Gorria
Arrate Pereda
Blanca Gener
Laura Garcia-Naveda
Guiomar Perez de Nanclares
机构
[1] OSI Araba University Hospital,Rare Diseases Research Group. Molecular (Epi)Genetics Laboratory, BioAraba Health Research Institute
[2] Faculty of Pharmacy,Laboratory of Pharmacy and Pharmaceutical Technology
[3] University of the Basque Country (UPV/EHU),Service of Genetics, BioCruces Bizkaia Health Research Institute
[4] Hospital Universitario Cruces,Service of Pediatric Neurology, BioAraba Health Research Institute
[5] Hospital Universitario Araba-Txagorritxu,undefined
来源
BMC Medical Genomics | / 11卷
关键词
Silver-Russell syndrome; Cri-du-chat syndrome; aCGH; Deletion;
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[1]  
Silver HK(1953)Syndrome of congenital hemihypertrophy, shortness of stature, and elevated urinary gonadotropins Pediatrics 12 368-376
[2]  
Kiyasu W(1954)A syndrome of intra-uterine dwarfism recognizable at birth with cranio-facial dysostosis, disproportionately short arms, and other anomalies (5 examples) Proc R Soc Med 47 1040-1044
[3]  
George J(2017)Diagnosis and management of Silver-Russell syndrome: first international consensus statement Nat Rev Endocrinol Nature Publishing Group 13 105-124
[4]  
Deamer WC(1990)Three-generation dominant transmission of the Silver-Russell syndrome Am J Med Genet 35 245-250
[5]  
Russell A(2015)A prospective study validating a clinical scoring system and demonstrating phenotypical-genotypical correlations in Silver-Russell syndrome J Med Genet 52 446-453
[6]  
Wakeling EL(2013)CDKN1C mutation affecting the PCNA-binding domain as a cause of familial Russell Silver syndrome J Med Genet 50 823-830
[7]  
Brioude F(2015)Paternally inherited IGF2 mutation and growth restriction N Engl J Med 373 349-356
[8]  
Lokulo-Sodipe O(2018)Structural and sequence variants in patients with Silver-Russell syndrome or similar features-curation of a disease database Hum Mutat 39 345-364
[9]  
O’Connell SM(2017)De novo mutation of paternal IGF2 gene causing Silver-Russell syndrome in a sporadic patient Front Genet 8 105-293
[10]  
Salem J(2015)A splicing mutation of the HMGA2 gene is associated with Silver-Russell syndrome phenotype J Hum Genet 60 287-535