Idiopathic infantile arterial calcification: clinical presentation, therapy and long-term follow-up

被引:0
作者
Inge M. van der Sluis
Annemieke M. Boot
Meike Vernooij
Morteza Meradji
André A. Kroon
机构
[1] Sophia Children’s Hospital,Department of Paediatrics, Erasmus Medical Centre
[2] Sophia Children’s Hospital,Division of Endocrinology, Erasmus Medical Centre
[3] Sophia Children’s Hospital,Department of Paediatric Radiology, Erasmus Medical Centre
[4] Sophia Children’s Hospital,Division of Neonatology, Erasmus Medical Centre
来源
European Journal of Pediatrics | 2006年 / 165卷
关键词
Idiopathic infantile arterial calcification; Bisphosphonates; Therapy; Diagnostics; Long-term follow-up;
D O I
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中图分类号
学科分类号
摘要
Idiopathic infantile arterial calcification (IIAC) is a rare disease characterised by extensive depositions of hydroxyapatite in the internal elastic lamina of medium-sized and large arteries, frequently accompanied by periarticular calcifications. We report on three patients with various presenting signs and symptoms. Diagnostic imaging techniques and therapy with bisphosphonates will be discussed. For the first time long-term follow-up of up to 25 years will be reported.
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页码:590 / 593
页数:3
相关论文
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