Evaluation and Management of Left Ventricular Noncompaction Cardiomyopathy

被引：11
作者：
Stacey R.B. [1 ]
Caine A.J. [1 ]
Jr [1 ]
Hundley W.G. [1 ,2 ]
机构：
[1] Department of Internal Medicine Section on Cardiology, Wake Forest University School of Medicine, Winston-Salem, 27157, NC
[2] Department Radiology, Wake Forest University School of Medicine, Winston-Salem, 27157, NC
来源：
Current Heart Failure Reports | 2015年 / 12卷 / 1期
关键词：
Cardiac magnetic resonance imaging; Congestive heart failure; Echocardiography; Embolic events; Noncompaction cardiomyopathy; Sudden cardiac death;
D O I：
10.1007/s11897-014-0237-1
中图分类号：
学科分类号：
摘要：
Left ventricular (LV) noncompaction cardiomyopathy (LVNC) is a form of cardiomyopathy in which trabeculations fail to “compact” with the left ventricular endocardium during fetal cardiac development and is classically associated with subsequent impairment of LV function, significant mortality, ventricular dysrhythmias, and embolic phenomena. As awareness and medical imaging quality have improved, it is becoming easier to identify trabeculations that traverse the LV cavity and serve as a distinguishing feature of this disorder. Differentiating true noncompaction from mild increases in trabeculations requires prudent imaging and clinical correlation. This review seeks to discuss the potential methods of evaluating left ventricular trabeculations, the role of increased trabeculations in cardiovascular disease, and how their presence may affect clinical management. © 2014, Springer Science+Business Media New York.
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收藏
页码：61 / 67
页数：6
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