Pulmonary arteriovenous malformations: a clinical review

被引：40
作者：
Iqbal, M
Rossoff, LJ
Steinberg, HN
Marzouk, KA
Siegel, DN
机构：
[1] Long Isl Jewish Med Ctr, Albert Einstein Coll Med, Div Pulm & Crit Care Med, New Hyde Pk, NY 11042 USA
[2] Long Isl Jewish Med Ctr, Div Vasc & Intervent Radiol, New Hyde Pk, NY 11042 USA
来源：
POSTGRADUATE MEDICAL JOURNAL | 2000年 / 76卷 / 897期
关键词：
arteriovenous malformation; hypoxaemia; shunt study; embolisation;
D O I：
10.1136/pmj.76.897.390
中图分类号：
R5 [内科学];
学科分类号：
1002 ; 100201 ;
摘要：
Pulmonary arteriovenous malformations (PAVMs) are a rare clinical entity. Most of them are associated with hereditary haemorrhagic telangiectasia. The usual clinical presentation is exertional dyspnoea and hypoxaemia. The initial test of choice for screening is the 100% oxygen method. A pulmonary angiogram is needed to define the anatomy and guide transcatheter embolisation (TCE). TCE has been shown to be effective and safe with a very low recanalisation rate and has largely replaced surgery for PAVMs. Computed tomography of the chest can be used for the follow up of asymptomatic PAVMs and TCE.
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收藏
页码：390 / 394
页数：5
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