Nephroblastomatosis and Wilms tumour: report of 2 cases.

被引:0
作者
Jouini, R [1 ]
Maazoun, K [1 ]
Chelly, S [1 ]
Mekki, M [1 ]
Belgnith, M [1 ]
Nouri, A [1 ]
机构
[1] Hop Univ Fattouma Bourguiba, Serv Chirurg Pediat, Monastir 5000, Tunisia
来源
PROGRES EN UROLOGIE | 2003年 / 13卷 / 02期
关键词
Wilms tumour; nephroblastomatosis; child;
D O I
暂无
中图分类号
R5 [内科学]; R69 [泌尿科学(泌尿生殖系疾病)];
学科分类号
1002 ; 100201 ;
摘要
Nephroblastomatosis is a rare disease, considered to be a precursor of Wilms tumour When it is isolated, recommended treatment consists of chemotherapy followed by surveillance. In the presence of associated Wilms tumour treatment consists of preoperative chemotherapy followed by partial nephrectomy (when possible), followed by postoperative chemotherapy and surveillance.
引用
收藏
页码:273 / 276
页数:4
相关论文
共 16 条
[1]  
Bagnulo S, 1994, Pediatr Med Chir, V16, P95
[2]  
BECKWITH J B, 1990, Pediatric Pathology, V10, P1
[3]  
BRESLOW N, 1988, CANCER RES, V48, P1653
[4]   NEPHROBLASTOMATOSIS - COMPARISON OF CT WITH US AND UROGRAPHY [J].
FERNBACH, SK ;
FEINSTEIN, KA ;
DONALDSON, JS ;
BAUM, ES .
RADIOLOGY, 1988, 166 (01) :153-156
[5]   NEPHROBLASTOMATOSIS - CLINICOPATHOLOGIC SIGNIFICANCE AND IMAGING CHARACTERISTICS [J].
FRANKEN, EA ;
YIUCHIU, V ;
SMITH, WL ;
CHIU, LC .
AMERICAN JOURNAL OF ROENTGENOLOGY, 1982, 138 (05) :950-952
[6]   Nephron-sparing surgery in synchronous bilateral Wilms' tumors [J].
Fuchs, J ;
Wünsch, L ;
Flemming, P ;
Weinel, P ;
Mildenberger, H .
JOURNAL OF PEDIATRIC SURGERY, 1999, 34 (10) :1505-1509
[7]  
HADDY TB, 1997, J PEDIATR, V90, P784
[8]  
HEIDEMAN RL, 1985, CANCER-AM CANCER SOC, V55, P1446, DOI 10.1002/1097-0142(19850401)55:7<1446::AID-CNCR2820550704>3.0.CO
[9]  
2-5
[10]   CLINICOPATHOLOGIC FEATURES OF NEPHROBLASTOMATOSIS [J].
HENNIGAR, RA ;
OTHERSEN, HB ;
GARVIN, AJ .
UROLOGY, 1989, 33 (04) :259-270