Isolated noncompaction involving the left ventricular apex in adults

被引:13
作者
Chung, T
Yiannikas, J
Lee, LCL
Lau, GT
Kritharides, L
机构
[1] Univ Sydney, Dept Cardiol, Concord Hosp, Sydney, NSW 2006, Australia
[2] Prince Wales Hosp, Dept Cardiol, Sydney, NSW, Australia
[3] Univ New S Wales, Ctr Vasc Res, Sydney, NSW, Australia
关键词
D O I
10.1016/j.amjcard.2004.07.102
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
We present a series of 9 adults in 2 families with isolated noncompaction of the ventricular myocardium involving the left ventricular apex. Three of these patients had been previously misdiagnosed as having dilated cardiomyopathy, apical hypertrophic cardiomyopathy, or apical mural thrombus. Pheno-typic variation was observed with gradation of severity of noncompaction and left ventricular systolic dysfunction between first-degree relatives. (C) 2004 by Excerpta Medica, Inc.
引用
收藏
页码:1214 / 1216
页数:3
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