Abnormally low ratio of cholic acid to chenodeoxycholic acid due to a deficiency of 3-oxo-Δ4-steroid 5β-reductase

被引：6

作者：

Kimura, A ^{[1
]}

Nittono, H

Takei, H

Kurosawa, T

机构：

[1] Kurume Univ, Sch Med, Dept Pediat & Child Hlth, Fukuoka 8300011, Japan

[2] Junshin Clin, Yokohama, Kanagawa, Japan

[3] Tokyo Hlth Serv Assoc, Tokyo, Japan

[4] Hlth Sci Univ Hokkaido, Fac Pharmaceut Sci, Hokkaido, Japan

来源：

PEDIATRICS INTERNATIONAL | 2000年 / 42卷 / 05期

关键词：

D O I：

10.1046/j.1442-200x.2000.01284.x

中图分类号：

R72 [儿科学];

学科分类号：

100202 ;

摘要：

引用

页码：594 / 594

页数：1

共 5 条

[1] Delta(4)-3-Oxosteroid 5 beta-reductase deficiency: Failure of ursodeoxycholic acid treatment and response to chenodeoxycholic acid plus cholic acid [J].

Clayton, PT ;

Mills, KA ;

Johnson, AW ;

Barabino, A ;

Marazzi, MG .

GUT, 1996, 38 (04) :623-628

[2] Urinary 7α-hydroxy-3-oxochol-4-en-24-oic and 3-oxachola-4,6-dien-24-oic acids in infants with cholestasis [J].

Kimura, A ;

Suzuki, M ;

Murai, T ;

Kurosawa, T ;

Tohma, M ;

Sata, M ;

Inoue, T ;

Hoshiyama, A ;

Nakashima, E ;

Yamashita, Y ;

Fujisawa, T ;

Kato, H .

JOURNAL OF HEPATOLOGY, 1998, 28 (02) :270-279

[3] ABNORMAL LOW RATIO OF CHOLIC-ACID TO CHENODEOXYCHOLIC ACID IN A CHOLESTATIC INFANT WITH SEVERE HYPOGLYCEMIA [J].

KIMURA, A ;

YUGE, K ;

YUKIZANE, S ;

KAGE, M ;

NITTONO, H ;

MAHARA, R ;

KUROSAWA, T ;

TOHMA, M .

JOURNAL OF PEDIATRIC GASTROENTEROLOGY AND NUTRITION, 1991, 12 (03) :383-387

[4]

SETCHELL KDR, 1994, LIVER DIS CHILDREN, P835

[5] THE URINARY BILE-ACID EXCRETION IN HEALTHY PREMATURE AND FULL-TERM INFANTS DURING THE NEONATAL-PERIOD [J].

STRANDVIK, B ;

WAHLEN, E ;

WIKSTROM, SA .

SCANDINAVIAN JOURNAL OF CLINICAL & LABORATORY INVESTIGATION, 1994, 54 (01) :1-10

← 1 →