Infantile motor neuron disease with autonomic dysfunction and bunina bodies

被引：0
作者：
Semmekrot, BA
Wesseling, P
Bruinenberg, JFM
Gabreels, FM
ter Laak, H
Sengers, RCA
机构：
[1] Univ Nijmegen Hosp, Dept Pediat, Div Neonatol, NL-6500 HB Nijmegen, Netherlands
[2] Univ Nijmegen Hosp, Dept Pathol, NL-6500 HB Nijmegen, Netherlands
[3] Univ Nijmegen Hosp, Dept Child Neurol, NL-6500 HB Nijmegen, Netherlands
[4] Univ Nijmegen Hosp, Dept Neurol, NL-6500 HB Nijmegen, Netherlands
来源：
ACTA NEUROPATHOLOGICA | 1998年 / 95卷 / 01期
关键词：
infant; bunina bodies; autonomic dysfunction; motor neuron disease; amyotrophic lateral sclerosis;
D O I：
10.1007/s004010050771
中图分类号：
R74 [神经病学与精神病学];
学科分类号：
摘要：
A 2-month-old girl developed motor neuron disease (MND) with autonomic disturbances and died al the age of 5 months. Neuropathological examination revealed Bunina bodies (BBs) in the lower motor neurons of the lumbar spinal cord. The significance of the presence of BBs and the classification of the MND in this child are discussed.
引用
收藏
页码：104 / 106
页数：3
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