A Rare Case of Solitary Giant Congenital Juvenile Xanthogranuloma: A Case Report

被引：7

作者：

Vignault, Catherine ^{[1
]}

Bourgeault, Emilie ^{[2
]}

Gagne, Eric ^{[2
]}

Bujold, Janie ^{[3
]}

机构：

[1] Univ Sherbrooke, Sherbrooke, PQ, Canada

[2] Hotel Dieu Quebec, Quebec City, PQ, Canada

[3] Hop Maria, Maria, PQ, Canada

来源：

JOURNAL OF CUTANEOUS MEDICINE AND SURGERY | 2017年 / 21卷 / 03期

关键词：

xanthogranuloma; juvenile; giant; congenital; non-Langerhans cell histiocytosis; PLAQUE;

D O I：

10.1177/1203475417690718

中图分类号：

R75 [皮肤病学与性病学];

学科分类号：

100206 ;

摘要：

Juvenile xanthogranuloma (JXG) is the most frequent form of non-Langerhans cell histiocytosis. We present a case of giant congenital JXG in a 7-week-old boy, who had a firm and incompressible lesion, measuring 3 x 4 cm in diameter, on his right flank. The clinical appearance of the lesion and the ultrasound results suggested a vascular tumor, such as a hemangioma. Histology confirmed a JXG, although there was an absence of Touton cells, which are usually pathognomonic of JXG. In light of these findings, it would be important to include JXG in the differential diagnosis of congenital tumours, particularly vascular lesions.

引用

页码：267 / 269

页数：3

共 15 条

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