CT and MR imaging of Susac syndrome in a young male presenting with acute disorientation

被引:19
作者
Allmendinger, Andrew M. [1 ]
Spektor, Vadim [1 ]
Destian, Sylvie [1 ]
机构
[1] St Vincent Catholic Med Ctr, New York, NY 10011 USA
关键词
MRI; Brain; Microangiopathy; Corpus callosum; Encephalopathy; MICROANGIOPATHY; RETINA; BRAIN;
D O I
10.1016/j.clinimag.2009.09.003
中图分类号
R8 [特种医学]; R445 [影像诊断学];
学科分类号
1002 ; 100207 ; 1009 ;
摘要
Susac syndrome is a rare neurologic disorder first described by Susac et al in 1979 Clinically, Susac syndrome consists of a triad including encephalopathy, branch retinal artery occlusion, and sensorineural hearing loss Microinfarction is believed to be the basic histologic feature and MR is considered the best imaging modality This case documents the typical imaging findings of Susac syndrome, as well as the unique MR imaging finding of cranial nerve enhancement (C) 2010 Elsevier Inc All rights reserved
引用
收藏
页码:138 / 142
页数:5
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