Sanjad-Sakati Syndrome: Oral Health Care

被引：6
作者：
Hassona, Yazan [1 ,2 ,4 ]
Rajab, Lamis [3 ,4 ]
Taimeh, Dina [1 ,2 ,4 ]
Scully, Crispian [5 ]
机构：
[1] Univ Jordan, Sch Dent, Dept Oral & Maxillofacial Surg, Amman, Jordan
[2] Univ Jordan, Sch Dent, Dept Oral Med & Periodontol, Amman, Jordan
[3] Univ Jordan, Sch Dent, Pediat Dent & Orthodont, Amman, Jordan
[4] Univ Jordan Hosp, Dept Dent, Amman, Jordan
[5] UCL, London, England
来源：
MEDICAL PRINCIPLES AND PRACTICE | 2018年 / 27卷 / 03期
关键词：
Sanjad-Sakati syndrome; Dental health care; Hypoparathyroidism; Mental retardation; Learning disability; Seizure disorder; FEATURES;
D O I：
10.1159/000488352
中图分类号：
R5 [内科学];
学科分类号：
1002 ; 100201 ;
摘要：
Objectives: The aim of this report is to describe the orofacial manifestations and dental management of a girl with Sanjad-Sakati syndrome. Clinical Presentation and Intervention: The facial features included microcephaly, thin lips, beaked nose, low set ears, and a retrognathic mandible. An oral examination revealed oligodontia/hypodontia, small dental arches, a high arched palate, and a deep overbite and increased overjet. Oral rehabilitation involved full coverage prosthetic crowns on the upper central incisors, stainless steel crowns on the lower molars, and removable partial prostheses to replace missing teeth. Conclusion: Recognition of orofacial features might help in the diagnosis of Sanjad-Sakati syndrome. Dental management of affected patients might be complicated by intellectual, neurological, and endocrine abnormalities. (C) 2018 The Author(s) Published by S. Karger AG, Basel
引用
收藏
页码：293 / 296
页数：4
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