Importance of Absent Ductus Arteriosus in Tetralogy of Fallot with Absent Pulmonary Valve Syndrome

被引:10
作者
Qureshi, Muhammad Yasir [1 ]
Burkhart, Harold M. [2 ]
Julsrud, Paul [3 ]
Cetta, Frank [1 ]
机构
[1] Mayo Clin, Div Pediat Cardiol, Rochester, MN 55905 USA
[2] Mayo Clin, Div Cardiovasc Surg, Rochester, MN 55905 USA
[3] Mayo Clin, Div Cardiovasc Radiol, Rochester, MN 55905 USA
关键词
Aorta/abnormalities; ductus arteriosus/abnormalities; heart defects; congenital/complications/diagnosis/genetics/surgery; infant; pulmonary valve/abnormalities; respiratory insufficiency/etiology; subclavian artery/abnormalities; tetralogy of Fallot/complications; INTACT VENTRICULAR SEPTUM; RIGHT AORTIC-ARCH; NATURAL-HISTORY; ANOMALIES; DEFECT;
D O I
10.14503/THIJ-13-3674
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Tetralogy of Fallot without pulmonary valve syndrome is almost always associated with an absent ductus arteriosus. Patients with right aortic arch and retroesophageal left subclavian artery have a vascular ring if the left ductus arteriosus or its remnant and the Kommerell diverticulum are present. We report the cases of 2 infants in whom the role of an absent ductus arteriosus or its remnant is noteworthy. Both patients had a combination of tetralogy of Fallot with absent pulmonary valve syndrome and right aortic arch with retroesophageal left subclavian artery without a vascular ring. The absence of the ductus arteriosus has a role in the pathogenesis of tetralogy of Fallot with absent pulmonary valve syndrome. The absence of a ductus arteriosus in the right aortic arch with retroesophageal left subclavian artery precludes a vascular ring.
引用
收藏
页码:664 / 667
页数:4
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