Primary Sjogren's syndrome: a great masquerader

被引:4
作者
Kumar, Naveen [1 ]
Surendran, Deepanjali [1 ]
Srinivas, Bheemanathi Hanuman [2 ]
Bammigatti, Chanaveerappa [1 ]
机构
[1] Jawaharlal Inst Post Grad Med Educ, Med, Pondicherry, India
[2] Jawaharlal Inst Post Grad Med Educ & Res, Pathol, Pondicherry, India
关键词
dentistry and oral medicine; peripheral nerve disease; Sjogren's syndrome;
D O I
10.1136/bcr-2019-231802
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
A 41-year-old woman presented with paresthesia and inability to walk for 7 days. She had history of fatigue, polyarthralgia and difficulty in swallowing food for the last 1year. She became edentulous over the last 5 years and wore dentures for the same. She appeared pale, emaciated and had oral thrush. She had areflexic quadriparesis with weakness more in lower limbs compared with upper limbs. With the initial diagnosis of Guillian-Barre syndrome, she was given five cycles of plasmapheresis following which there was a significant improvement in power. Sjogren's syndrome was suspected based on edentulous state in a middle-aged woman with multisystem involvement. Evaluation with Schirmer's test, parotid scintigraphy and labial minor salivary gland biopsy confirmed the diagnosis. She was treated with steroids following which a dramatic improvement in haemoglobin and total leucocyte count was noted. We report a varied presentation of primary Sjogren's syndrome.
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页数:4
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