The natural history of thoracolumbar kyphosis in achondroplasia

被引:15
作者
Ahmed, Malik [1 ]
El-Makhy, Mahmoud [1 ]
Grevitt, Michael [1 ]
机构
[1] Nottingham Univ Hosp NHS Trust, Ctr Spinal Studies & Surg, Queens Med Ctr Campus,Derby Rd, Nottingham NG7 2UH, England
关键词
Achondroplasia; Thoracolumbar kyphosis; Bone dysplasias; Gibbus; SURGICAL-TREATMENT; GROWTH;
D O I
10.1007/s00586-016-4861-1
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
There are little published data on the natural history and evolution of thoracolumbar kyphotic deformity in achondroplasia. Furthermore, there are few published reports indicating the probability of symptoms and at what kyphotic angle progressive deformity might occur. The lack of knowledge of the fundamental natural history does not allow firm guidelines for the management of this problem. In this respect the role of bracing remains uncertain both in terms of altering the prognosis for further vertebral wedging and overall sagittal profile. This report describes three illustrative cases of thoracolumbar kyphosis (TLK) that occurred in achondroplastic infants. The long-term outcomes are presented to illustrate the diverse clinical behaviour of TLK in this patient group.
引用
收藏
页码:2602 / 2607
页数:6
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