Spindle cell embryonal rhabdomyosarcoma of the prostate in an adult patient - case report and review of clinicopathological features

被引:10
作者
Schildhaus, Hans-Ulrich [1 ]
Lokka, Suvi [2 ]
Fenner, Werner [3 ]
Kuester, Jens [3 ]
Kuehnle, Ingrid [4 ]
Heinmoeller, Ernst [2 ]
机构
[1] Univ Med Ctr Gottingen, Dept Pathol, Gottingen, Germany
[2] Inst Pathol Nordhessen, Germaniastr 7, D-34119 Kassel, Germany
[3] Nephrol Zentrum, Dept Urol, Vogelsang 105, D-34346 Munden, Germany
[4] Univ Med Ctr Gottingen, Dept Pediat Hematol & Oncol, Gottingen, Germany
关键词
Embryonal rhabdomyosarcoma; Prostate; Adults; SARCOMA; CLASSIFICATION; EXPERIENCE; VARIANT;
D O I
10.1186/s13000-016-0507-1
中图分类号
R36 [病理学];
学科分类号
100104 ;
摘要
Background: Embryonal rhabdomyosarcoma of the prostate in an adult is a very rare event with only a few cases published. Diagnosis usually occurs with advanced disease frequently already with metastatic spread. In adults prognosis is very poor, therefore early diagnosis is crucial. To date, only three cases of spindle cell subtype of embryonal rhabdomyosarcoma of the prostate in an adult have been published. Case presentation: We report an additional case of prostatic spindle cell embryonal rhabdomyosarcoma subtype in an adult. Conclusions: We discuss relevant clinicopathological features of spindle cell embryonal rhabdomyosarcoma of the prostate in adult patients in the context of the literature.
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页数:5
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