Multiple Intestinal Intussusceptions in Peutz-Jeghers' Syndrome : a Case Report

被引：1

作者：

Basak, F. ^{[1
]}

Kinaci, E. ^{[1
]}

Aksoy, S. ^{[1
]}

Sevinc, M. ^{[1
]}

Aren, A. ^{[1
]}

机构：

[1] TC SB Istanbul Educ & Res Hosp, Dept Gen Surg, Konya, Turkey

来源：

ACTA CHIRURGICA BELGICA | 2010年 / 110卷 / 01期

关键词：

Intussusception; Peutz-Jeghers syndrome; short bowel syndrome; CANCER; RISK;

D O I：

10.1080/00015458.2010.11680575

中图分类号：

R61 [外科手术学];

学科分类号：

摘要：

Peutz-Jeghers' syndrome (PJS) is an autosomal dominant inherited disease, which is characterized by mucocutaneus pigmentation and hamartomatous gastro-intestinal polyps. Intussusceptions call easily occur ill patients with PJS. Repeated laparotomy with resections and eventual short bowel syndrome is a major problem in these patients. We present a 20-year-old woman with multiple intestinal intussusceptions. Multiple enterotomics and intestinal resections were performed to achieve a longer symptom-free period.

引用

页码：93 / 94

页数：2

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