A rare case of association between Budd-Chiari syndrome and sea-blue histiocytosis

被引：1

作者：

Hu, F. ^{[1
]}

Zhang, Y. ^{[1
]}

Yi, Z. ^{[1
]}

机构：

[1] Sichuan Univ, Dept Gastroenterol, West China Hosp, 37 Guoxue Alley, Chengdu, Sichuan, Peoples R China

来源：

NIGERIAN JOURNAL OF CLINICAL PRACTICE | 2019年 / 22卷 / 11期

关键词：

Bone marrow aspiration and biopsy; Budd-Chiari syndrome; hepatosplenomegaly; portal hypertension; sea-blue histiocytosis; INFERIOR VENA-CAVA; MEMBRANOUS OBSTRUCTION; BONE-MARROW; INVOLVEMENT; SECONDARY; ETIOLOGY;

D O I：

10.4103/njcp.njcp_43_19

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

Budd-Chiari syndrome (BCS) is a rare disease characterized by obstruction of hepatic venous outflow tract with diversified etiologies. Sea-blue histiocytosis (SBH) is a kind of storage diseases defined by the deposition of abundant sea-blue histiocytes in various organs and can lead to hepatosplenomegaly, cirrhosis, or even liver failure. The association between BCS and SBH has never been reported before. Here, we report a patient with BCS presenting with hepatosplenomegaly, portal hypertension, and pancytopenia who was later confirmed to also have SBH.

引用

页码：1617 / 1620

页数：4

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