Ascending aorta aneurysm in scleroderma

被引:0
作者
Chintala, Bhavya [1 ]
Duggal, Lalit [1 ]
Jain, Neeraj [1 ]
机构
[1] Sir Ganga Ram Hosp, Dept Rheumatol & Clin Immunol, Room 2208 A,SSRB Block, New Delhi 110060, India
关键词
Ascending aorta; aneurysm; scleroderma; SYSTEMIC-SCLEROSIS; DISEASE;
D O I
10.1177/23971983211023322
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Ascending aorta aneurysm in scleroderma can be ascribed to its macrovascular involvement which is very less elucidated. We here describe a 56-year-old female with rapidly progressive diffuse cutaneous scleroderma. She presented with skin thickening involving all four limbs, thorax and abdomen. She had other features like arthritis, Raynaud's phenomena, dyspnoea, heaviness of chest, and dysphagia. On investigation, she was strongly positive for antinuclear antibody and Scl 70. Imaging revealed interstitial lung disease (nonspecific interstitial pneumonia pattern) and a fusiform dilatation of ascending aorta of 6.5 cm. Patient was offered surgical correction for aneurysm, for which she refused. To the best of our knowledge, our case report adds up to the few cases of ascending aorta aneurysm in scleroderma available in world literature.
引用
收藏
页码:322 / 326
页数:5
相关论文
共 14 条
[1]   Scleroderma: from cell and molecular mechanisms to disease models [J].
Abraham, DJ ;
Varga, J .
TRENDS IN IMMUNOLOGY, 2005, 26 (11) :587-595
[2]   Assessment of vascular function in systemic sclerosis -: Indications of the development of nitrate tolerance as a result of enhanced endothelial nitric oxide production [J].
Andersen, G ;
Mincheva-Nilsson, L ;
Kazzam, E ;
Nyberg, G ;
Klintland, N ;
Petersson, AS ;
Rantapää-Dahlqvist, S ;
Waldenström, A ;
Caidahl, K .
ARTHRITIS AND RHEUMATISM, 2002, 46 (05) :1324-1332
[3]   Ascending aortic aneurysm in a man with scleroderma [J].
Attaran, Robert R. ;
Guarraia, David .
CLINICAL RHEUMATOLOGY, 2007, 26 (06) :1027-1028
[4]   Carotid and femoral arterial wall mechanics in scleroderma [J].
Cheng, KS ;
Tiwari, A ;
Boutin, A ;
Denton, CP ;
Black, CM ;
Morris, R ;
Hamilton, G ;
Seifalian, AM .
RHEUMATOLOGY, 2003, 42 (11) :1299-1305
[5]   Macrovascular disease and systemic sclerosis [J].
Ho, ML ;
Veale, D ;
Eastmond, C ;
Nuki, G ;
Belch, J .
ANNALS OF THE RHEUMATIC DISEASES, 2000, 59 (01) :39-43
[6]   Raynaud phenomenon and the vascular disease in scleroderma [J].
Kahaleh, MB .
CURRENT OPINION IN RHEUMATOLOGY, 2004, 16 (06) :718-722
[7]   Cerebral aneurysms in scleroderma [J].
Kaku, Y ;
Kouda, K ;
Yoshimura, S ;
Sakai, N .
CEREBROVASCULAR DISEASES, 2004, 17 (04) :339-341
[8]   THE MORPHOLOGY OF ASCENDING AORTIC-ANEURYSMS [J].
KLIMA, T ;
SPJUT, HJ ;
COELHO, A ;
GRAY, AG ;
WUKASCH, DC ;
REUL, GJ ;
COOLEY, DA .
HUMAN PATHOLOGY, 1983, 14 (09) :810-817
[9]  
KOCH AE, 1990, AM J PATHOL, V137, P1199
[10]   Ultrasonographic screening for abdominal aortic aneurysms [J].
Lederle, FA .
ANNALS OF INTERNAL MEDICINE, 2003, 139 (06) :516-522