Erythrodermic syringotropic cutaneous T-cell lymphoma

被引:5
作者
Ah-Weng, A
Howatson, SR
Goodlad, JR
Patel, MC
Gupta, G
机构
[1] Monklands Hosp, Dept Dermatol, Airdrie, Lanark, Scotland
[2] Monklands Hosp, Dept Pathol, Airdrie, Lanark, Scotland
[3] Raigmore Hosp, Dept Pathol, Inverness, Scotland
关键词
cutaneous T-cell lymphoma; interferon alfa; methotrexate; mycosis fungoides; syringolymphoid hyperplasia; syringotropic cutaneous T-cell lymphoma;
D O I
10.1046/j.1365-2133.2003.05187.x
中图分类号
R75 [皮肤病学与性病学];
学科分类号
100206 ;
摘要
Syringotropic cutaneous T-cell lymphoma (CTCL) is a rare localized variant of CTCL, characterized histologically by eccrine gland and ductal hyperplasia surrounded by a dense syringotropic lymphocytic infiltrate. Previously reported only in men, we describe the first woman with syringotropic CTCL. Unusually, she presented with erythroderma, cutaneous nodules, poikilodermatous patches, widespread alopecia and lymphadenopathy.
引用
收藏
页码:349 / 352
页数:4
相关论文
共 9 条
[1]   ECCRINE PROLIFERATION WITH FOLLICULAR MUCINOSIS [J].
BERGER, TG ;
GOETTE, DK .
JOURNAL OF CUTANEOUS PATHOLOGY, 1987, 14 (03) :188-190
[2]   SYRINGOLYMPHOID HYPERPLASIA WITH ALOPECIA - A SYRINGOTROPIC CUTANEOU T-CELL LYMPHOMA [J].
BURG, G ;
SCHMOCKEL, C .
DERMATOLOGY, 1992, 184 (04) :306-307
[3]   Further evidence that syringolymphoid hyperplasia with alopecia is a cutaneous T-cell lymphoma [J].
Esche, C ;
Sander, CA ;
Zumdick, M ;
Kutzner, H ;
Kind, P ;
Schulte, K ;
Ruzicka, T ;
Lehmann, P .
ARCHIVES OF DERMATOLOGY, 1998, 134 (06) :753-754
[4]   PATCHY ALOPECIA ANHIDROSIS ECCRINE GLAND WALL HYPERTROPHY AND VASCULITIS [J].
SARKANY, I .
PROCEEDINGS OF THE ROYAL SOCIETY OF MEDICINE-LONDON, 1969, 62 (02) :157-&
[5]   Syringolymphoid hyperplasia and follicular mucinosis in a patient with cutaneous T-cell lymphoma [J].
Tannous, Z ;
Baldassano, MF ;
Li, VW ;
Kvedar, J ;
Duncan, LM .
JOURNAL OF THE AMERICAN ACADEMY OF DERMATOLOGY, 1999, 41 (02) :303-308
[6]  
TOMASZEWSKI MM, 1994, J CUTAN PATHOL, V21, P520
[7]   SYRINGOLYMPHOID HYPERPLASIA WITH ALOPECIA [J].
VAKILZADEH, F ;
BROCKER, EB .
BRITISH JOURNAL OF DERMATOLOGY, 1984, 110 (01) :95-101
[8]   MYCOSIS-FUNGOIDES IN THE UNITED-STATES - INCREASING INCIDENCE AND DESCRIPTIVE EPIDEMIOLOGY [J].
WEINSTOCK, MA ;
HORM, JW .
JAMA-JOURNAL OF THE AMERICAN MEDICAL ASSOCIATION, 1988, 260 (01) :42-46
[9]   SYRINGOTROPIC CUTANEOUS T-CELL LYMPHOMA - A VARIANT OF MYCOSIS-FUNGOIDES [J].
ZELGER, B ;
SEPP, N ;
WEYRER, K ;
GRUNEWALD, K ;
ZELGER, B .
BRITISH JOURNAL OF DERMATOLOGY, 1994, 130 (06) :765-769