Glanzmann's thrombasthenia proposed optimal management during surgery and delivery

被引：19

作者：

Bell, JA ^{[1
]}

Savidge, GF ^{[1
]}

机构：

[1] St Thomas Hosp, Haemophilia Reference Ctr, Ctr Haemostasis & Thrombosis, London SE1 7EH, England

来源：

CLINICAL AND APPLIED THROMBOSIS-HEMOSTASIS | 2003年 / 9卷 / 02期

关键词：

thrombasthenia; platelet refractoriness; surgery; pregnancy; rVIIa (Novoseven (R));

D O I：

10.1177/107602960300900213

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

Glanzmann's thrombasthenia (GT) is an autosomal recessive disorder of platelet function. Conventional management is by platelet transfusion, given before invasive interventions. Alloimmunization resulting in platelet refractoriness and an unpredictable response to platelet infusion have provided particular management difficulties in the past. More recently recombinant (r)VIIa (Novoseven((R))) has a valuable role in the treatment of platelet function disorders. Treatment of a patient with GT during two pregnancies and spinal surgery is reported. An algorithm is presented to provide a structured and consistent approach to treatment.

引用

页码：167 / 170

页数：4

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