SECONDARY IMMUNE THROMBOCYTOPENIA IN THE PRIMARY IMMUNODEFICIENCY DISORDER IN ADULT HEMATOLOGICAL PRACTICE

Thrombocytopenia is a symptom of a wide range of hematological and non-hematological diseases, requiring extensive diagnostic search. Rapid detection of the main cause of thrombocytopenia affects the prognosis and therapeutic tactics in a number of patients with hematological diseases. One of the reasons for the development of secondary thrombocytopenia are primary immunodeficiency disorders (PID), whose debut is possible at the age of over 18 years. Diagnosis of this pathology is difficult, due to the low alertness of primary care physicians about the presence of favorably occurring primary immunodeficiencies, the first manifestation of which can be the immune thrombocytopenia revealed in an adult. This article is devoted to the report of the clinical cases of newly diagnosed PID in adulthood, debuting from autoimmune complications.