Malignant Familial Adenomatous Polyposis treated by Laparoscopic Colectomy and Ileal Pouch Anal Anastomosis: a Case Report

被引：0

作者：

Zaharie, Florin ^{[1
,2
]}

Ciorogar, George ^{[1
,2
]}

Zaharie, Roxana ^{[2
,3
]}

Tantau, Marcel ^{[2
,3
]}

Iancu, Cornel ^{[1
,3
]}

Mocan, Lucian ^{[1
,3
]}

机构：

[1] Iuliu Hatieganu Univ Med & Pharm, Surg Clin 3, Cluj Napoca 400162, Romania

[2] Prof Dr Octavian Fodor Reg Inst Gastroenterol & H, Cluj Napoca, Romania

[3] Iuliu Hatieganu Univ Med & Pharm, Med Cin 3, Cluj Napoca 400162, Romania

来源：

JOURNAL OF GASTROINTESTINAL AND LIVER DISEASES | 2014年 / 23卷 / 04期

关键词：

familial adenomatous polyposis; laparoscopic proctocolectomy; malignant polyposis; J pouch; RESTORATIVE PROCTOCOLECTOMY; SURVEILLANCE; CHILDREN; DISEASE; CANCER; BOWEL;

D O I：

暂无

中图分类号：

R57 [消化系及腹部疾病];

学科分类号：

摘要：

The mean age of colorectal cancer in untreated familial adenomatous polyposis (FAP) is 39 years. We present the case of a 21-year-old patient with FAP and colorectal cancer. The patient was detected with significant family history: her mother died at age 45 with colon cancer; two uncles were diagnosed with colon cancer at the age of 40 and 43 and one aunt at the age of 45 with colon cancer and gastric cancer. The treatment was laparoscopic restorative proctocolectomy with total excision of the mesorectum and heal pouch anal anastomosis completed with endoanal excision of inferior rectal polyps. The histopathological report described a well differentiated rectal adenocarcinoma T1N1aMx developed on a tubulo-villous adenoma located on the rectosigmoid jonction, the rest of the polyps with benign histology.

引用

页码：445 / 448

页数：4

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