Anti-epiligrin (laminin 5) cicatricial pemphigoid

被引:13
作者
Allbritton, JI [1 ]
Nousari, HC [1 ]
Anhalt, GJ [1 ]
机构
[1] Johns Hopkins Hosp, Dept Dermatol, Baltimore, MD 21287 USA
关键词
D O I
10.1111/j.1365-2133.1997.tb01566.x
中图分类号
R75 [皮肤病学与性病学];
学科分类号
100206 ;
摘要
Cicatricial pemphigoid is an autoimmune disease predominantly of elderly patients. Recently, a subtype of cicatricial pemphigoid with antibodies to epiligrin (laminin 5) was described. We report a patient in whom anti-epiligrin cicatricial pemphigoid was identified. He presented with cutaneous, oral and ocular involvement. He has shown initial improvement on corticosteroids and cyclophosphamide.
引用
收藏
页码:992 / 996
页数:5
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