More Than Epiphyseal Osteochondromas: Updated Understanding of Imaging Findings in Dysplasia Epiphysealis Hemimelica (Trevor Disease)

被引：10

作者：

Degnan, Andrew J. ^{[1
,2
]}

Ho-Fung, Victor M. ^{[1
,2
]}

机构：

[1] Childrens Hosp Philadelphia, Dept Radiol, 3NW39,3401 Civ Ctr Blvd, Philadelphia, PA 19104 USA

[2] Univ Penn, Perelman Sch Med, Dept Radiol, Philadelphia, PA 19104 USA

来源：

AMERICAN JOURNAL OF ROENTGENOLOGY | 2018年 / 211卷 / 04期

关键词：

dysplasia epiphysealis hemimelica; epiphyseal overgrowth; MRI; osteochondroma; skeletal dysplasia; Trevor disease; OF-THE-LITERATURE; EPIPHYSIALIS HEMIMELICA; MRI; METACHONDROMATOSIS; MANIFESTATIONS; INVOLVEMENT; DIAGNOSIS; KNEE; AFIP; LIMB;

D O I：

10.2214/AJR.18.19712

中图分类号：

R8 [特种医学]; R445 [影像诊断学];

学科分类号：

1002 ; 100207 ; 1009 ;

摘要：

OBJECTIVE. The purpose of this article is to discuss approaches to imaging dysplasia epiphysealis hemimelica in the context of recent advances in the understanding of the underlying pathophysiologic profile of this entity, which may result in pain, growth disturbance, and early development of osteoarthritis. CONCLUSION. Dysplasia epiphysealis hemimelica was first characterized as a skeletal disorder with osteochondromas characteristically involving epiphyses on one side of the same lower extremity. Upper extremity involvement was subsequently recognized. Previously conceptualized as epiphyseal osteochondromatosis, recent investigations have uncovered differences between these osteocartilaginous lesions and osteochondromas.

引用

页码：910 / 919

页数：10

共 43 条

[1] Dysplasia epiphysealis hemimelica in a young girl: role of MRI in the diagnosis and follow-up [J].