European Respiratory Society guidelines for the diagnosis and management of lymphangioleiomyomatosis

被引:376
作者
Johnson, S. R. [1 ,2 ]
Cordier, J. F. [3 ]
Lazor, R. [3 ,4 ]
Cottin, V. [3 ]
Costabel, U. [5 ]
Harari, S. [6 ]
Reynaud-Gaubert, M. [7 ]
Boehler, A. [8 ]
Brauner, M. [9 ]
Popper, H. [10 ]
Bonetti, F. [11 ]
Kingswood, C. [12 ]
机构
[1] Univ Nottingham, Div Therapeut & Mol Med, Queens Med Ctr, Nottingham NG7 2UH, England
[2] Univ Nottingham, Resp Biomed Res Unit, Nottingham NG7 2UH, England
[3] Univ Lyon 1, Reference Ctr Rare Pulm Dis, F-69365 Lyon, France
[4] CHU Vaudois, Clin Interstitial & Rare Lung Dis, Dept Resp Med, CH-1011 Lausanne, Switzerland
[5] Univ Klinikum Essen, Ruhrlandklin, Essen, Germany
[6] Osped San Giuseppe AFAR, Unit Pneumol, Milan, Italy
[7] St Marguerite Univ Hosp, Div Pulm Med & Thorac Surg, Marseille, France
[8] Univ Hosp, Pulm Med & Lung Transplant Program, Zurich, Switzerland
[9] Univ Paris, Serv Radiol, Hop Avicenne, Bobigny, France
[10] Graz Univ, Inst Pathol, A-8010 Graz, Austria
[11] Univ Verona, Policlin B Roma, I-37100 Verona, Italy
[12] Royal Sussex Cty Hosp, Brighton BN2 5BE, E Sussex, England
关键词
Angiomyolipoma; chylous effusions; cystic lung disease; lymphangioleiomyomatosis; pneumothorax; tuberous sclerosis; TUBEROUS SCLEROSIS COMPLEX; BLEEDING RENAL ANGIOMYOLIPOMA; SMOOTH-MUSCLE-CELLS; PULMONARY LYMPHANGIOLEIOMYOMATOSIS; LUNG TRANSPLANTATION; CHYLOUS ASCITES; FOLLOW-UP; LYMPHANGIOMYOMATOSIS; CT; PREGNANCY;
D O I
10.1183/09031936.00076209
中图分类号
R56 [呼吸系及胸部疾病];
学科分类号
摘要
[No abstract available]
引用
收藏
页码:14 / 26
页数:13
相关论文
共 112 条
  • [31] ATS statement: Guidelines for the six-minute walk test
    Crapo, RO
    Casaburi, R
    Coates, AL
    Enright, PL
    MacIntyre, NR
    McKay, RT
    Johnson, D
    Wanger, JS
    Zeballos, RJ
    Bittner, V
    Mottram, C
    [J]. AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE, 2002, 166 (01) : 111 - 117
  • [32] Sirolimus therapy in tuberous sclerosis or sporadic lymphangioleiomyomatosis
    Davies, D. Mark
    Johnson, Simon R.
    Tattersfield, Anne E.
    Kingswood, J. Chris
    Cox, Jane A.
    McCartney, Deborah L.
    Doyle, Tim
    Elmslie, Frances
    Saggar, Anand
    de Vries, Petrus J.
    Sampson, Julian R.
    [J]. NEW ENGLAND JOURNAL OF MEDICINE, 2008, 358 (02) : 200 - 203
  • [33] de la Fuente J, 1993, Eur J Med, V2, P377
  • [34] Desurmont S, 1996, REV MAL RESPIR, V13, P300
  • [35] DETTERBECK FC, 1995, ANN THORAC SURG, V60, P139
  • [36] Dickinson M, 1998, CLIN NEPHROL, V49, P281
  • [37] Druelle S., 1995, Revue de Pneumologie Clinique, V51, P284
  • [38] Renal lesion growth in children with tuberous sclerosis complex
    Ewalt, DH
    Sheffield, E
    Sparagana, SP
    Delgado, MR
    Roach, ES
    [J]. JOURNAL OF UROLOGY, 1998, 160 (01) : 141 - 145
  • [39] Mutational and radiographic analysis of pulmonary disease consistent with lymphangioleiomyomatosis and micronodular pneumocyte hyperplasia in women with tuberous sclerosis
    Franz, DN
    Brody, A
    Meyer, C
    Leonard, J
    Chuck, G
    Dabora, S
    Sethuraman, G
    Colby, TV
    Kwiatkowski, DJ
    McCormack, FX
    [J]. AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE, 2001, 164 (04) : 661 - 668
  • [40] Fujimoto M, 2005, Clin Exp Obstet Gynecol, V32, P199