Development of renal and iliac aneurysms in a child with generalized infantile myofibromatosis

被引：12

作者：

Brasseur, Benoit ^{[1
,2
]}

Chantrain, Christophe F. ^{[1
]}

Godefroid, Nathalie ^{[3
]}

Sluysmans, Thierry ^{[4
]}

Anslot, Christine ^{[5
]}

Menten, Renaud

Clapuyt, Philippe

Dupont, Sophie ^{[1
]}

Vermylen, Christiane ^{[1
]}

Brichard, Benweicte ^{[1
]}

机构：

[1] Catholic Univ Louvain, Dept Pediat Hematol & Oncol, Clin Univ St Luc, B-1200 Brussels, Belgium

[2] Clin St Pierre, Dept Pediat, B-1340 Ottignies, Belgium

[3] Catholic Univ Louvain, Dept Pediat Nephrol, Clin Univ St Luc, B-1200 Brussels, Belgium

[4] Catholic Univ Louvain, Dept Pediat Cardiol, Clin Univ St Luc, B-1200 Brussels, Belgium

[5] Catholic Univ Louvain, Dept Pediat Intens Care, Clin Univ St Luc, B-1200 Brussels, Belgium

来源：

PEDIATRIC NEPHROLOGY | 2010年 / 25卷 / 05期

关键词：

Infantile myofibromatosis; Fibromuscular dysplasia; Renovascular hypertension; Aneurysm; Mesenchymal disorder; FIBROMUSCULAR DYSPLASIA; HYPERTENSION;

D O I：

10.1007/s00467-009-1393-5

中图分类号：

R72 [儿科学];

学科分类号：

100202 ;

摘要：

Infantile myofibromatosis is a rare disorder characterized by the formation of tumors in the skin, soft tissues, bone, and viscera. We report the case of a 3-week-old girl who presented with severe hypertension due to generalized infantile myofibromatosis including renal involvement. The infant was treated by chemotherapy and showed progressive regression of the tumors. However, her evolution was marked by the development of aneurismal dilations of the renal and iliac arteries as observed in fibromuscular dysplasia. We discuss the possibility of a link between these two mesenchymal disorders.

引用

页码：983 / 986

页数：4

共 12 条

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